CausalSentinel

Protein Dossier — GAA (Lysosomal alpha-glucosidase)

MR feasibility tier: A — Published pQTL-MR estimates exist for this protein (retrieved below - not computed here).

1. Published MR estimates (retrieved, not computed)

Outcome beta se p method nSNP cis/trans coloc
LDL cholesterol -0.0398 0.0146 0.00648 Wald ratio 1 cis NA
Serum cystatin C (eGFRcys) 0.0138 0.00515 0.00727 Wald ratio 1 cis NA
Non-cancer illness code self-reported: pernicious anaemia 0.258 0.0967 0.00764 Wald ratio 1 cis NA
Heel bone mineral density (BMD) T-score automated -0.0224 0.00869 0.01 Wald ratio 1 cis NA
Total cholesterol -0.0369 0.0144 0.0103 Wald ratio 1 cis NA
Type 2 diabetes -0.0801 0.0334 0.0165 Wald ratio 1 cis NA
Low grade serous ovarian cancer 0.311 0.134 0.0201 Wald ratio 1 cis NA
Fractured bone site(s): Wrist 0.101 0.0434 0.0202 Wald ratio 1 cis NA
Forced expiratory volume in 1-second (FEV1) 0.0135 0.00581 0.0203 Wald ratio 1 cis NA
Non-cancer illness code self-reported: bladder problem (not cancer) -0.261 0.116 0.0246 Wald ratio 1 cis NA
Sodium in urine -0.0146 0.00661 0.0271 Wald ratio 1 cis NA
Non-cancer illness code self-reported: vaginal prolapse or uterine prolapse 0.165 0.0777 0.0337 Wald ratio 1 cis NA
…and 94 more outcomes (see JSON)              

2. pQTL instrument availability (Tier-B probe)

No prot-* pQTL GWAS dataset found for this protein (matched by UniProt accession and symbol).

3. GWAS Catalog results — traits with signal at this locus

42 association rows across 27 traits (37 genome-wide significant rows). Associations are loci, not causal claims; the mapped gene at a locus is not necessarily the effector gene.

Trait best p lead SNP n assoc study MR status
Lysosomal alpha-glucosidase levels 3e-375 rs2304849 3 GCST90248358 no MR -> candidate analysis
Serum levels of protein GAA 4e-85 rs2304849 1 GCST90090674 no MR -> candidate analysis
Blood protein levels 1e-48 rs12450199 1 GCST006585 no MR -> candidate analysis
SGSH protein levels 9e-33 rs143436385 3 GCST90470615 no MR -> candidate analysis
Mean corpuscular hemoglobin concentration 4e-28 rs12451471 3 GCST90002391 no MR -> candidate analysis
Hematological traits (multi-trait analysis) 5e-27 rs12451471 1 GCST90838671 no MR -> candidate analysis
Height 2e-24 rs3816257 1 GCST90245848 MR: beta=0.00759, p=0.351 (cis)
Platelet distribution width (UKB data field 30110) 4e-19 rs3816257 1 GCST90468097 no MR -> candidate analysis
Mean corpuscular haemoglobin concentration (UKB data field 3 8e-19 rs12451471 1 GCST90468085 no MR -> candidate analysis
High light scatter reticulocyte percentage of red cells 2e-16 rs149900590 1 GCST90002386 no MR -> candidate analysis
Plateletcrit 1e-15 rs3834976 2 GCST90002400 no MR -> candidate analysis
High light scatter reticulocyte count 1e-15 rs149900590 1 GCST90002385 no MR -> candidate analysis
…and 15 more traits (see JSON)          

4. Phenome map — where this gene is a genetic locus, vs. where MR exists

Top diseases by Open Targets association (of 2642 total). Associations are loci, not causal claims. The causal-status column is a four-state triage per pair: established (curated) = a curated clinical assertion exists (ClinGen/G2P/GEL/Orphanet/ClinVar — any validity level, MR adds little); exploratory rare-variant signal = ExWAS burden evidence without curation — a candidate NEW gene-disease relationship; common-variant locus = GWAS signal, classic pQTL-MR territory; multi-layer = burden+GWAS together, an allelic-series candidate (the strongest causal setup). Burden estimand is carrier-vs-noncarrier, not per-SD MR.

Disease genetic assoc. burden (ExWAS) causal status MR status
Glycogen storage disease due to acid maltase deficiency 0.989 established (curated) no MR -> candidate analysis
glycogen storage disease II 0.989 established (curated) no MR -> candidate analysis
glycogen storage disease due to acid maltase deficiency, infantile onset 0.525 established (curated) no MR -> candidate analysis
glycogen storage disease due to acid maltase deficiency, late-onset 0.821 established (curated) no MR -> candidate analysis
disorder of glycogen metabolism 0.864 established (curated) no MR -> candidate analysis
Abnormality of the cardiovascular system 0.885 established (curated) no MR -> candidate analysis
myopathy 0.559 established (curated) no MR -> candidate analysis
glycogen storage disease due to glycogen branching enzyme deficiency 0.559 established (curated) no MR -> candidate analysis
Elevated circulating creatine kinase concentration 0.547 established (curated) no MR -> candidate analysis
hereditary disease 0.559 established (curated) no MR -> candidate analysis
glycoprotein storage disease 0.559 established (curated) no MR -> candidate analysis
glycogen storage disease due to glucose-6-phosphatase deficiency type IA 0.547 established (curated) no MR -> candidate analysis
Acute rhabdomyolysis 0.438 established (curated) no MR -> candidate analysis
Rare genetic deafness 0.438 established (curated) no MR -> candidate analysis
Abnormality of metabolism/homeostasis 0.438 established (curated) no MR -> candidate analysis

Of the 15 rows above, 15 have no MR estimate in this resource. Across all retrieved diseases for this gene: 0 exploratory rare-variant signal(s), 0 multi-layer (allelic-series candidate) pair(s). Final triage still belongs to a statistical geneticist.

5. Downstream annotation (druggability & safety preview)

Layer Result
ChEMBL druggability 2 known modulators (Lysosomal alpha-glucosidase)
gnomAD constraint pLI=1.7e-25, LOEUF=1.01 — LoF-tolerant
GWAS Catalog 89 unique SNPs / 178 rows
ClinVar 3676 records; 22 pathogenic in sample of 30
PharmGKB/ClinPGx no annotations

Caveats declared by the tools

Sources

Provenance