CausalSentinel

Protein Dossier — XRCC4 (DNA repair protein XRCC4)

MR feasibility tier: A — Published pQTL-MR estimates exist for this protein (retrieved below - not computed here).

1. Published MR estimates (retrieved, not computed)

Outcome beta se p method nSNP cis/trans coloc
Lung adenocarcinoma 0.411 0.147 0.00522 Wald ratio 1 trans NA
Forearm bone mineral density 0.216 0.0782 0.00581 Wald ratio 1 trans NA
Ulcerative colitis -0.145 0.0616 0.0187 Wald ratio 1 trans NA
Total cholesterol 0.044 0.0191 0.0211 Wald ratio 1 trans NA
Serum cystatin C (eGFRcys) -0.0199 0.00896 0.0266 Wald ratio 1 trans NA
Lung cancer 0.219 0.102 0.0315 Wald ratio 1 trans NA
Crohn’s disease 0.122 0.0598 0.0414 Wald ratio 1 trans NA
Red blood cell count -0.023 0.0113 0.0419 Wald ratio 1 trans NA
HDL cholesterol 0.037 0.0183 0.0433 Wald ratio 1 trans NA
Rheumatoid arthritis 0.227 0.113 0.0439 Wald ratio 1 trans NA
Neuroticism -0.0312 0.0156 0.0455 Wald ratio 1 trans NA
Internalizing problems -0.191 0.107 0.0743 Wald ratio 1 trans NA
…and 40 more outcomes (see JSON)              

2. pQTL instrument availability (Tier-B probe)

No prot-* pQTL GWAS dataset found for this protein (matched by UniProt accession and symbol).

3. GWAS Catalog results — traits with signal at this locus

65 association rows across 28 traits (55 genome-wide significant rows). Associations are loci, not causal claims; the mapped gene at a locus is not necessarily the effector gene.

Trait best p lead SNP n assoc study MR status
VCAN protein levels 1e-94 rs2441009 6 GCST90471032 no MR -> candidate analysis
DNA repair protein XRCC4 levels 2e-22 rs11953364 1 GCST90250224 no MR -> candidate analysis
XRCC4 protein levels 2e-20 rs1805377 1 GCST90471085 no MR -> candidate analysis
Cerebellar grey matter morphology (MOSTest) 2e-17 rs1478486 1 GCST90728589 no MR -> candidate analysis
IDP dMRI TBSS ICVF Middle cerebellar peduncle 5e-17 rs10473864 1 GCST90004327 no MR -> candidate analysis
heart rate (HR, mean, inv-normal transformed) 8e-14 rs17284253 1 GCST90480666 no MR -> candidate analysis
heart rate (HR, minimum, inv-normal transformed) 4e-12 rs17284253 1 GCST90476341 no MR -> candidate analysis
IDP dMRI TBSS ICVF Fornix cres+Stria terminalis R 9e-12 rs4343818 1 GCST90004365 no MR -> candidate analysis
Heel bone mineral density 3e-11 rs10474093 3 GCST007066 no MR -> candidate analysis
White matter microstructure (mean diusivities) 7e-11 rs2591453 20 GCST009538 no MR -> candidate analysis
White matter microstructure (radial diusivities) 2e-10 rs10055352 10 GCST009540 no MR -> candidate analysis
IDP dMRI TBSS ICVF Superior longitudinal fasciculus R 3e-10 rs10473864 1 GCST90004367 no MR -> candidate analysis
…and 16 more traits (see JSON)          

4. Phenome map — where this gene is a genetic locus, vs. where MR exists

Top diseases by Open Targets association (of 286 total). Associations are loci, not causal claims. The causal-status column is a four-state triage per pair: established (curated) = a curated clinical assertion exists (ClinGen/G2P/GEL/Orphanet/ClinVar — any validity level, MR adds little); exploratory rare-variant signal = ExWAS burden evidence without curation — a candidate NEW gene-disease relationship; common-variant locus = GWAS signal, classic pQTL-MR territory; multi-layer = burden+GWAS together, an allelic-series candidate (the strongest causal setup). Burden estimand is carrier-vs-noncarrier, not per-SD MR.

Disease genetic assoc. burden (ExWAS) causal status MR status
microcephalic primordial dwarfism-insulin resistance syndrome 0.864 established (curated) no MR -> candidate analysis
short stature, microcephaly, and endocrine dysfunction 0.911 established (curated) no MR -> candidate analysis
Non-acquired isolated growth hormone deficiency 0.547 established (curated) no MR -> candidate analysis
androgenetic alopecia 0.455 common-variant locus no MR -> candidate analysis
dyshidrosis 0.443 common-variant locus no MR -> candidate analysis
multinodular goiter 0.42 common-variant locus no MR -> candidate analysis
endometriosis 0.391 common-variant locus no MR -> candidate analysis
rheumatoid arthritis 0.375 common-variant locus MR: beta=0.227, p=0.0439 (trans)
head and neck cancer 0.335 common-variant locus no MR -> candidate analysis
aging 0.336 common-variant locus no MR -> candidate analysis
Abnormality of the gastrointestinal tract 0.329 common-variant locus no MR -> candidate analysis
hereditary disease 0.313 established (curated) no MR -> candidate analysis
skin neoplasm 0.311 common-variant locus no MR -> candidate analysis
subarachnoid hemorrhage 0.308 common-variant locus no MR -> candidate analysis
facial morphology 0.297 common-variant locus no MR -> candidate analysis

Of the 15 rows above, 14 have no MR estimate in this resource. Across all retrieved diseases for this gene: 0 exploratory rare-variant signal(s), 0 multi-layer (allelic-series candidate) pair(s). Final triage still belongs to a statistical geneticist.

5. Downstream annotation (druggability & safety preview)

Layer Result
ChEMBL druggability 0 known modulators (LIG4/XRCC4)
gnomAD constraint pLI=1.8e-07, LOEUF=0.982 — LoF-tolerant
GWAS Catalog 58 unique SNPs / 110 rows
ClinVar 215 records; 3 pathogenic in sample of 30
PharmGKB/ClinPGx 3 clinical annotations across 4 drugs

Caveats declared by the tools

Sources

Provenance